Abstract

INFANTILE SCAPULAR CAFFEY DISEASE-A CASE REPORT

Anjali Jayakumar*, Aleena Sunny, Ankitha George, S. Haja Sherief and T. Sivakumar

ABSTRACT

Caffey disease is congenital and genetic musculoskeletal disease that most commonly occur in babies. The condition is self limited without a defined cause. It is marked by an acute inflammation of the periosteum and is characterized by systemic changes of irritability and fever. The diagnosis of Caffey disease is often challenging as it is a genetic abnormality. It impersonate certain diseases mainly osteogenesis imperfecta, Ehlers-Danlos syndrome, hypervitaminosis A and Hurler syndrome. In most cases physician diagnose the disease through physical examination. The condition resolves within six months and no specific treatment is required. NSAID’s such as Indomethacin and Acetaminophen may be given to the patient as palliative treatment. We describe a case of one month old infant presented with swelling over the right shoulder.

Keywords: Caffey Disease, Infantile Cortical Hyperostosis, Periosteum.