Abstract

MAYER-ROKITANSKY-KUSTER-HAUSER SYNDROME CASE REPORT AND REVIEW OF THE LITERATURE

K. El Matar*, K. Tamim, A. Benani, S. Bargach, M. Elyousfi, A. Drissi Mniani, L. Chat, N. Allali and S. Elhaddad

ABSTRACT

Mayer-Rokitansky-kuster-Hauser syndrome or Mullerian aplasia, or uterovaginal aplasia is a rare congenital condition characterized by the absence of a uterus and at least the upper two-thirds of the vagina, a female phenotype and a karyotype 46 XX. Imaging is an essential step in making the diagnosis. And Whatever the therapeutic technique used, close monitoring should be considered as well as psychological support.

Keywords: Mayer-Rokitansky-kuster-Hauser syndrome, Imaging.